Priority 5 from the Liver Glycogen Storage Disease (International) PSP
| UNCERTAINTY: What is the best way to start dietary treatment, finding the optimal doses, and to administer the diet for patients with liver Glycogen Storage Disease? (JLA PSP Priority 5) | |
|---|---|
| Overall ranking | 5 |
| JLA question ID | 0090/5 |
| Explanatory note |
Dietary treatment for patients with liver GSD can be initiated via several options, depending on internal and external factors of the individual patient. |
| Evidence |
For details of the evidence checked, please see the spreadsheet held on the JLA website. |
| Health Research Classification System category | Metabolic and endocrine |
| Extra information provided by this PSP | |
|---|---|
| Original uncertainty examples | How frequently to recommend an in-hospital stay for adjustment of diet and cornstarch? ~ How best to administer cornstarch, timing with respect to meals? ~ Can the use of the gastric tube be forever? |
| Submitted by | Patient, carer and healthcare professionals |
| PSP information | |
|---|---|
| PSP unique ID | 0090 |
| PSP name | International Glycogen Storage Disease PSP |
| Total number of uncertainties identified by this PSP | 72 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website) |
| Date of priority setting workshop | 24 May 2019 |