Priority 19(joint) from the Liver Glycogen Storage Disease (International) PSP
| UNCERTAINTY: When should liver transplantation be considered in patients with liver Glycogen Storage Disease and what are the (dis)advantages and long-term outcomes? (JLA PSP Priority 19 (Joint)) | |
|---|---|
| Overall ranking | 19 |
| JLA question ID | 0090/19 (Joint) |
| Explanatory note |
Liver transplantation is a modality of treatment that is indicated for specific situations for patients with liver GSD. However, not much follow-up information on long-term outcomes are known. |
| Evidence |
For details of the evidence checked, please see the spreadsheet held on the JLA website. |
| Health Research Classification System category | Metabolic and endocrine |
| Extra information provided by this PSP | |
|---|---|
| Original uncertainty examples | When to consider liver or transplantation for best outcomes? ~ The role and timing of livertransplant in the treatment of GSDI/GSDIII. ~ When is transplant indicated in the absence of significant fibrosis or a tumor? ~ Particular care of these patients in the pre- and post-liver transplantation |
| Submitted by | Patient, carer and healthcare professionals |
| PSP information | |
|---|---|
| PSP unique ID | 0090 |
| PSP name | International Glycogen Storage Disease PSP |
| Total number of uncertainties identified by this PSP | 72 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website) |
| Date of priority setting workshop | 24 May 2019 |