Priority 19(joint) from the Liver Glycogen Storage Disease (International) PSP
| UNCERTAINTY: How to prevent and/or treat hormonal problems (i.e. thyroid, menstrual cycle, growth, diabetes, insulin response) in patients with liver Glycogen Storage Disease? (JLA PSP Priority 19 (Joint)) | |
|---|---|
| Overall ranking | 19 (Joint) |
| JLA question ID | 0090/19 (Joint) |
| Explanatory note |
As treatment of liver GSD is further optimized these past decades, the liver GSD cohort is ageing. As such, long-term complications associated with liver GSD and its treatment can be investigated further. |
| Evidence |
For details of the evidence checked, please see the spreadsheet held on the JLA website. |
| Health Research Classification System category | Metabolic and endocrine |
| Extra information provided by this PSP | |
|---|---|
| Original uncertainty examples | Risk of developing concurrent diabetes ~ What are the long term effects from stress on the body due to GSD? ~ How big is the inference between GSD and hormones in female patients? ~ insuline reponse in gsd? |
| Submitted by | Patient, carer and healthcare professionals |
| PSP information | |
|---|---|
| PSP unique ID | 0090 |
| PSP name | International Glycogen Storage Disease PSP |
| Total number of uncertainties identified by this PSP | 72 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website) |
| Date of priority setting workshop | 24 May 2019 |