Priority 17 from the Liver Glycogen Storage Disease (International) PSP
| UNCERTAINTY: How can patients with liver Glycogen Storage Disease achieve and/or maintain a healthy weight throughout life? (JLA PSP Priority 17) | |
|---|---|
| Overall ranking | 17 |
| JLA question ID | 0090/17 |
| Explanatory note |
Weight gain can be a complication of liver GSD since the cornerstone of treatment is a diet rich in complex carbohydrates. This question emphasized that more research is necessary on protocols to prevent, achieve or maintain a healthy weight, without metabolic derangement occuring due to undertreatment. |
| Evidence |
For details of the evidence checked, please see the spreadsheet held on the JLA website. |
| Health Research Classification System category | Metabolic and endocrine |
| Extra information provided by this PSP | |
|---|---|
| Original uncertainty examples | Development of overweight and diabetes at an adult age. ~ The weight gain that comes with consuming cornstarch ~ Is there a possibility to lose weight despite the high carbohydrates? |
| Submitted by | Patient, carer and healthcare professionals |
| PSP information | |
|---|---|
| PSP unique ID | 0090 |
| PSP name | International Glycogen Storage Disease PSP |
| Total number of uncertainties identified by this PSP | 72 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website) |
| Date of priority setting workshop | 24 May 2019 |