Priority 16 from the Liver Glycogen Storage Disease (International) PSP
| UNCERTAINTY: What is the needed restriction of lactose, fructose or saccharose in different types of liver Glycogen Storage Disease? (JLA PSP Priority 16) | |
|---|---|
| Overall ranking | 16 |
| JLA question ID | 0090/16 |
| Explanatory note |
Guidelines emphasize that lactose, fructose and saccharose are carbohydrates that are have to be strictly avoided in GSD Type I. |
| Evidence |
For details of the evidence checked, please see the spreadsheet held on the JLA website. |
| Health Research Classification System category | Metabolic and endocrine |
| Extra information provided by this PSP | |
|---|---|
| Original uncertainty examples | I would like to know retriction of fructose and galactose restriction. What is the best way to go? ~ Can my son have limited amounts of lactose and fructose? I get different answers depending who I speak to. He is type 1A. ~ Can we clear the diet from adolescence concerning lactose and fructose without risk. |
| Submitted by | Patient, carer and healthcare professionals |
| PSP information | |
|---|---|
| PSP unique ID | 0090 |
| PSP name | International Glycogen Storage Disease PSP |
| Total number of uncertainties identified by this PSP | 72 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website) |
| Date of priority setting workshop | 24 May 2019 |